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Jakob–Creutzfeldt disease

Jakob–Creutzfeldt disease Jakob–Creutzfeldt disease is a rare transmissible brain disorder that most often appears between ages 50 and 70 and causes rapidly worsening neurological and mental changes, such as sleep problems, personality change, movement abnormalities, language problems, visual loss, progressive dementia, and usually death within a year of onset.

Jakob–Creutzfeldt disease is a rare transmissible brain disorder that most often appears between ages 50 and 70 and causes rapidly worsening neurological and mental changes, such as sleep problems, personality change, movement abnormalities, language problems, visual loss, progressive dementia, and usually death within a year of onset. Familial and variant forms have also been described, and the disease is marked by spongiform brain degeneration and prions.